A Rare and Massive Primitive Neuroectodermal Tumour

Primitive neuroectodermal tumours was originally described by Askin et al. [1]. It is commonly found in children and young females. It frequently appears as a chest wall mass and grows rapidly to involve the neighboring pleura. The histogenesis of this rare tumour is uncertain and it is believed to be arising from the intercostal nerves. It exclusively arises from one hemi thorax and progresses rapidly to involve the chest wall. Involvement of the mediastinum in the adult is extremely rare in the literature and till now only five such cases in a span of twenty years have been reported from a tertiary care centre of India [2]. We herein report the sixth case of an anterior mediastinal PNET in an adult female which had progressed rapidly to a huge mass involving the entire left hemithorax and measuring the heaviest PNET reported so far in the literature, (Table 1).